Web(11) Michel B: Hailey-Hailey disease--familial benign chronic pemphigus. Arch Derm 118: 781-783, 1982 (12) Malchus R et al. HLA-B 16 in Hailey-Hailey's disease. Acta Derm … WebBenign chronic familial pemphigus (Hailey-Hailey disease) is a rare autosomal dominant blistering skin disorder characterized by suprabasal cell separation (acantholysis) of the …
Familial Benign Pemphigus (Hailey-Hailey Disease) - Medscape
Benign familial pemphigus is also known as Hailey–Hailey disease. It is a rare hereditaryblistering skin disease first described by the Hailey brothers in 1939. Unrelated to pemphigus vulgaris, Hailey-Hailey disease is not an autoimmune condition and has a differing prognosis. See more Benign familial pemphigus usually appears in the second to fourth decade, although it can occur at any age. It then tends to persistlife-long. It can affect people of all races. See more Benign familial pemphigus typically begins as a symmetrical painful erosive and crusted skin rash in the skin folds. Common sites include the armpits, groins, and neck, under the breasts and between the buttocks. The … See more Benign familial pemphigus is an inherited skin disorder, although occasionally sporadic cases arise without a family history. The defect responsible has now been identified on a … See more For many patients benign familial pemphigus is a mild condition, but for others, the pain and smell can be serious … See more WebHailey–Hailey disease, or familial benign chronic pemphigus: 559 or familial benign pemphigus,: 622 was originally described by the Hailey brothers (Hugh Edward and … royal road levels
Familial Benign Pemphigus (Hailey-Hailey Disease) Treatment
WebJan 1, 1995 · A patient with benign familial chronic pemphigus was treated with cyclosporin at a dose ranging from 2.8 to 3.4 mg/kg per day and there was a clear improvement in the area of skin affected and in exudation and soreness. A patient with benign familial chronic pemphigus was treated with cyclosporin at a dose ranging from … WebJul 7, 2024 · Familial benign pemphigus (Hailey-Hailey disease) originally was described by the Hailey brothers in 1939. Familial benign pemphigus is a chronic autosomal … WebWe describe a 25-year-old woman with multiple papules in the perianal and perineal area, clinically resembling condylomata acuminata. The histology revealed an acantholytic epidermis and focal parakeratosis. The lesions were diagnosed as Hailey-Hailey disease localized in the perianal areal and need … royal road latest